Tri atressia  Anterior frontal view of the opened heart. White arrows indicate normal blood flow. Tricuspid valve labeled at bottom left. Medical genetics Tricuspid atresia is a form of congenital heart disease whereby there is a complete absence of the tricuspid valve. Therefore, there is an absence of right atrioventricular connection. This leads to a hypoplastic undersized or absent right ventricle.
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Tricuspid atresia may be diagnosed during pregnancy or soon after a baby is born. During Pregnancy During pregnancy, there are screening tests also called prenatal tests to check for birth defects and other conditions. Tricuspid atresia might be seen during an ultrasound which creates pictures of the body. Some findings from the ultrasound may make the health care provider suspect that a baby might have tricuspid atresia.
If so, the health care provider can request a fetal echocardiogram to confirm the diagnosis. This test can show problems with the structure of the heart and how the heart is working with this defect. After a Baby is Born Babies born with tricuspid atresia will show symptoms at birth or very soon afterwards. Infants with tricuspid atresia can have additional symptoms such as: Problems breathing Ashen or bluish skin color Poor feeding Extreme sleepiness During a physical examination, a doctor can see the symptoms, such as bluish skin or problems breathing.
However, it is not uncommon for a heart murmur to be absent right at birth. If a doctor suspects that there might be a problem, the doctor can request one or more tests to confirm the diagnosis of tricuspid atresia. The most common test is an echocardiogram. This is an ultrasound of the heart that can show problems with the structure of the heart, like holes in the walls between the chambers, and any irregular blood flow.
Cardiac catheterization inserting a thin tube into a blood vessel and guiding it to the heart also can confirm the diagnosis by looking at the inside of the heart and measuring the blood pressure and oxygen. An electrocardiogram EKG , which measures the electrical activity of the heart, and other medical tests may also be used to make the diagnosis. Tricuspid atresia is a critical congenital heart defect critical CHD that also can be detected with newborn screening using pulse oximetry also known as pulse ox.
Low levels of oxygen in the blood can be a sign of a critical CHD. Newborn screening using pulse oximetry can identify some infants with a critical CHD, like tricuspid atresia, before they show any symptoms. Treatment Medicines Some babies and children will need medicines to help strengthen the heart muscle, lower their blood pressure, and help the body get rid of extra fluid. Nutrition Some babies with tricuspid atresia become tired while feeding and do not eat enough to gain weight.
To make sure babies have a healthy weight gain, a special high-calorie formula might be prescribed. Some babies become extremely tired while feeding and might need to be fed through a feeding tube. Surgery Surgical treatment for tricuspid atresia depends on its severity and presence of other heart defects. Soon after a baby with tricuspid atresia is born, one or more surgeries may be needed to increase blood flow to the lungs and bypass the poorly functioning right side of the heart.
Other surgeries or procedures may be needed later. These surgeries, described below, do not cure tricuspid atresia, but they help restore heart function. Sometimes medicines are given to help treat symptoms of the defect before or after surgery. This is done so that more oxygen-poor blood can mix with oxygen-rich blood, so that more oxygen-rich blood can get to the body. Banding If the baby has other heart defects along with tricuspid atresia, sometimes there is too much blood flowing to the lungs and not enough going out to the rest of the body.
Too much blood in the lungs can damage them. This banding is a temporary procedure and will likely be removed. Surgeons create a bypass shunt from the aorta to the main pulmonary artery, allowing blood to get to the lungs. If the aorta is small, as occurs when the baby also has transposition of the great arteries, the surgeon will also enlarge the aorta at this time.
Bi-directional Glenn Procedure This usually is performed when an infant is 4 to 6 months of age. This procedure creates a direct connection between the main pulmonary artery and the superior vena cava, the vessel returning oxygen-poor blood from the upper part of the body to the heart.
This allows blood returning from the body to flow directly to the lungs and bypass the heart. Fontan Procedure This procedure usually is done sometime around 2 years of age. Doctors connect the main pulmonary artery and the inferior vena cava, the vessel returning oxygen-poor blood from the lower part of the body to the heart, allowing the rest of the blood coming back from the body to go to the lungs.
Infants who have these surgeries are not cured; they might have lifelong complications. If the tricuspid atresia is very complex, or the heart becomes weak after the surgeries, a heart transplant might be needed.
An infant or child who receives a heart transplant will need to take medicines for the rest of his or her life to prevent the body from rejecting the new heart.
Babies born with tricuspid atresia will need regular follow-up visits with a cardiologist a heart doctor to monitor their progress and check for other health conditions that might develop as they get older. As adults, they may need more surgery or medical care for other possible problems. National population-based estimates for major birth defects, Birth Defects Res ; 1— Tricuspid Atresia The images are in the public domain and thus free of any copyright restrictions.
As a matter of courtesy we request that the content provider Centers for Disease Control and Prevention, National Center on Birth Defects and Developmental Disabilities be credited and notified in any public or private usage of this image. Close Tricuspid Atresia Comparison The images are in the public domain and thus free of any copyright restrictions. Close Page last reviewed: November 12,
Facts about Tricuspid Atresia
Atresia da válvula tricúspide